the parents of a 3 yo boy who has duchenne muscular dystrophy dmd ask how can our son have this disease we are wondering if we should have any more ch
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Nursing Elites

HESI RN

HESI Practice Test Pediatrics

1. What information should the nurse provide the parents of a 3-year-old boy with Duchenne muscular dystrophy (DMD) who are concerned about having more children?

Correct answer: A

Rationale: The correct answer is A. Duchenne muscular dystrophy is an inherited X-linked recessive disorder that primarily affects male children in the family. Since it is X-linked, sons inherit the mutation from their mothers who are carriers of the abnormal gene. Therefore, the nurse should explain to the parents that any future sons they have would have a 50% chance of inheriting the mutation and having DMD, while daughters would have a 50% chance of being carriers like the mother.

2. A 5-year-old child is brought to the emergency department with severe abdominal pain and vomiting. The child’s parent reports that the pain started suddenly and is located in the lower right abdomen. What should the nurse do first?

Correct answer: B

Rationale: The correct answer is to notify the healthcare provider immediately. The child's presentation of sudden, severe abdominal pain in the lower right abdomen is highly concerning for appendicitis, a medical emergency. Promptly notifying the healthcare provider is crucial for further evaluation and management. Administering pain medication as the first action might mask symptoms and delay diagnosis. Starting an IV line for fluid administration and obtaining a complete blood count are important interventions but should come after healthcare provider notification.

3. What action should the nurse implement when the infusion of chemotherapy via an implanted medication port is complete for a 16-year-old with acute myelocytic leukemia at the outpatient oncology clinic?

Correct answer: C

Rationale: The correct action for the nurse to implement when the chemotherapy infusion is complete is to flush the mediport with saline and heparin solution. This process helps prevent clotting and ensures the patency of the port, which is essential for future medication administrations and blood draws. Administering Zofran (Choice A) is not necessary after completing the chemotherapy infusion. Obtaining blood samples (Choice B) for RBCs, WBCs, and platelets is important but not the immediate action after completing the infusion. Initiating an infusion of normal saline (Choice D) is not required unless there is a specific indication for it.

4. A child with leukemia is admitted for chemotherapy, and the nursing diagnosis 'altered nutrition, less than body requirements related to anorexia, nausea, and vomiting' is identified. Which intervention should the nurse include in this child's plan of care?

Correct answer: B

Rationale: Allowing the child to eat any food desired and tolerated is the most appropriate intervention in this scenario. Anorexia, nausea, and vomiting are common side effects of chemotherapy, which can lead to altered nutrition. Allowing the child to choose foods they desire and can tolerate can help improve their nutritional intake during this challenging time. Encouraging large portions of food at every meal (Choice A) may overwhelm the child and worsen their symptoms. Eating like siblings at home (Choice C) may not align with the child's specific needs during chemotherapy. Restricting food from fast-food restaurants (Choice D) is not necessary as long as the food choices are suitable for the child's condition and preferences.

5. A 9-year-old child with a history of type 1 diabetes is brought to the clinic for a check-up. The nurse notes that the child's hemoglobin A1c is 8.5%. What is the most appropriate action for the nurse to take?

Correct answer: B

Rationale: A hemoglobin A1c of 8.5% indicates suboptimal diabetes control. The most appropriate action for the nurse in this scenario is to review the child’s dietary habits and insulin administration technique. This approach can help identify potential areas for improvement and optimize diabetes management, aiming to lower the hemoglobin A1c levels towards the target range. Increasing the child’s insulin dose (Choice A) without addressing dietary habits and administration technique may not lead to better control and can increase the risk of hypoglycemia. Switching to oral hypoglycemics (Choice C) is not appropriate for type 1 diabetes management. Scheduling a follow-up appointment in three months (Choice D) without intervening to improve diabetes control is not the best immediate action.

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