the parents of a 3 yo boy who has duchenne muscular dystrophy dmd ask how can our son have this disease we are wondering if we should have any more ch
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Nursing Elites

HESI RN

HESI Practice Test Pediatrics

1. What information should the nurse provide the parents of a 3-year-old boy with Duchenne muscular dystrophy (DMD) who are concerned about having more children?

Correct answer: A

Rationale: The correct answer is A. Duchenne muscular dystrophy is an inherited X-linked recessive disorder that primarily affects male children in the family. Since it is X-linked, sons inherit the mutation from their mothers who are carriers of the abnormal gene. Therefore, the nurse should explain to the parents that any future sons they have would have a 50% chance of inheriting the mutation and having DMD, while daughters would have a 50% chance of being carriers like the mother.

2. A child diagnosed with Kawasaki disease is brought to the clinic. The mother reports that her child is irritable, refuses to eat, and has skin peeling on both hands and feet. Which intervention should the nurse instruct the mother to implement first?

Correct answer: A

Rationale: Creating a quiet environment is the priority intervention as it helps reduce irritability and stress in children with Kawasaki disease. This intervention can promote a soothing atmosphere for the child, which may help in managing their symptoms effectively. Irritability and refusal to eat can be exacerbated by a noisy or stimulating environment. Making a list of foods the child likes is important, but addressing the immediate need for a calm environment takes precedence. Encouraging parents to rest is a good practice but not the immediate intervention needed for the child's symptoms. Applying lotion to hands and feet, although helpful for skin peeling, is not the first priority when dealing with irritability and refusal to eat.

3. A 16-year-old female student with a history of asthma controlled with both an oral antihistamine and an albuterol (ProAir) metered-dose inhaler (MDI) comes to the school nurse. The student complains that she cannot sleep at night, feels shaky, and her heart feels like it is 'beating a mile a minute.' Which information is most important for the nurse to obtain?

Correct answer: D

Rationale: The most crucial information for the nurse to obtain in this scenario is how often the metered-dose inhaler (MDI) is used daily. This information will help assess if the symptoms of insomnia, shakiness, and palpitations are potentially related to overuse of the inhaler, which can cause side effects such as tremors and palpitations. Monitoring the frequency of MDI usage is essential in managing asthma and ensuring appropriate medication administration.

4. A child with pertussis is receiving azithromycin (Zithromax Injection) IV. Which intervention is most important for the nurse to include in the child's plan of care?

Correct answer: C

Rationale: When administering azithromycin IV, monitoring for signs of an allergic reaction, such as facial swelling or urticaria, is crucial. This helps in early detection of potential adverse reactions and ensures prompt intervention to prevent complications associated with the medication. The other options are not directly related to the administration of azithromycin IV in this scenario. Monitoring for fluid overload would be more relevant for fluid administration, changing IV site dressing is important but not the priority in this case, and assessing for abdominal pain and vomiting may be important but not as critical as monitoring for signs of an allergic reaction.

5. Which drink choice on a hot day indicates that a teenager with sickle cell anemia understands dietary considerations related to the disease?

Correct answer: D

Rationale: Lemonade is the correct choice for a teenager with sickle cell anemia as it provides hydration without caffeine, which is important for individuals with this condition. Caffeine can lead to dehydration, vasoconstriction, and potentially worsen symptoms in sickle cell anemia patients. Milkshake (choice A) may contain dairy, which can be high in fat and may not be the best choice for someone with sickle cell anemia. Iced tea (choice B) and diet cola (choice C) both contain caffeine, which should be avoided by individuals with sickle cell anemia due to its dehydrating effects.

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